Understanding the Ear
To understand the types and causes of hearing
loss, it is helpful to understand the basic components of
the ear. The ear is divided into three main parts: the outer
ear, the middle ear, and the inner ear.
| Outer Ear: |
The outside of the ear, plus the ear
canal up to the eardrum or tympanic membrane. |
| Middle Ear: |
The cavity behind the tympanic membrane
which houses three small bones that help conduct sound
waves to the inner ear. |
| Inner Ear: |
The cavity behind the middle ear houses
a series of channels known as the labyrinth, and a snail-shaped
structure called the cochlea. The labyrinth is integral
to the human balance system. The cochlea contains the
thousands of nerves responsible for sensing sound and
transmitting it to the brain for processing. |
| Auditory Nerve: |
The eighth cranial nerve, which is the
pathway of sound from the ear to the brain. |
Types/Causes Of Hearing Loss
The type of hearing loss in any one person
depends upon where in the ear the problem occurs. Among
the common types of hearing loss are:
| Conductive: |
Loss of hearing caused by a problem
in the outer or middle ear. A conductive loss prevents
sound from reaching the nerves in the inner ear. Common
causes include:
- Deformity in the outer or middle ear structure.
- Ruptured eardrum.
- Wax buildup in the outer ear.
- Fluid buildup in the middle ear system.
|
| Sensorineural: |
Hearing loss caused by damage to some
or all of the nerves in the inner ear. Sensorineural
losses cannot be reduced or eliminated by surgery.
There are many causes, differing by age of onset.
Before or During Birth:
- Perinatal infections such as rubella, herpes, toxoplasmosis, syphilis,
cytomegalovirus (CMV)
- Heredity
- Asphyxia or lack of oxygen at birth.
- Possible association with birth weight of less
than 1500 grams.
- Possible association with defects of the head
and neck
Later Onset:
- Bacterial meningitis.
- Ototoxicity (drug induced).
- Intense or excessive noise.
- Physical damage to head or ear
|
| Mixed: |
Hearing loss caused by any combination
of the listed causes of conductive and sensorineural
hearing loss. |
Influence Of Varying Types Of Hearing Loss
Conductive Hearing Loss
Conductive hearing loss is generally a loudness difficulty.
In children with a conductive hearing loss, the inner ear system is intact
and ready to accept incoming sounds. The hearing loss is created by some
kind of blockage that prevents sound from reaching the functioning inner
ear. Once sound reaches the inner ear it is usually clear and undistorted.
Some implications of conductive loss are:
- The problem can usually be reduced or eliminated through
medical treatment.
- The problem may or may not be temporary, depending
on the nature of the blockage.
- If the hearing loss is of short duration, it should
have no effect on language learning. If the blockage is chronic or
repeated, it may influence speech and language development and educational
performance.
- If the loss is due to a long-term problem, and cannot
be resolved medically, habilitation may be necessary. Use of a hearing
aid may be recommended to overcome the blockage so the child does
not lose valuable language development and education time.
- Special Education programming is usually not necessary
for children with conductive hearing loss.
- Routine monitoring of hearing is recommended for children
who have repeated conductive or middle ear problems.
- Be aware that children who present classroom behavior
problems and appear to not pay attention may have fluctuating conductive
hearing loss.
Sensorineural Hearing Loss
Sensorineural hearing loss is a difficulty that involves
both distortion and loudness. Sensorineural loss may affect some or all
of the hair cells or nerves in the inner ear responsible for sensing
sounds of different pitches. This will cause varying degrees and configurations
of hearing loss. Several characteristics are typical of most sensorineural
hearing losses.
- The loss is permanent and cannot be surgically repaired.
- Early identification and intervention are necessary
to enable children who are deaf or hard of hearing to learn language
during the critical early years.
- Each deaf or hard of hearing child has unique language
learning and communication needs. Various language development and
educational approaches are chosen by families to address these needs.
- Hearing aids can benefit many children with sensorineural
loss. There are different levels of benefit a child may receive from
a hearing aid. Some children may benefit from a hearing aid to process
spoken English or components of spoken English while other children
may use a hearing aid only for more basic purposes such as alerting
to sounds.
Mixed Hearing Loss
Mixed hearing losses cause difficulty of both loudness
and distortion. Since mixed losses combine the characteristics of conductive
and sensorineural loss, the extent of each component will determine its
implications.
- If the conductive component is significant, with very
little damage to the nerves of the inner ear, the disorder will center
on loudness rather than distortion of sound.
- If the conductive component is minimal, with the sensorineural
component more significant, the loss may carry a larger distortion
factor.
- As conductive losses tend to fluctuate, depending
on the nature of the loss, mixed losses may also fluctuate and the
child's response behavior could vary from day to day.
Other Considerations:
- The age of onset of hearing loss has a significant
impact on a child's speech and language development. A child who
is prelingually deaf (became deaf before acquiring language) and
a child who is postlingually deaf (became deaf after exposure to
and acquisition of language) will each present different circumstances
in terms of language use and development.
- How quickly a child's hearing loss is diagnosed and
how expediently the child is provided access to a clear language
system will have a significant impact on the child's language development.
It should be noted that Deaf children from Deaf families who have
access to American Sign Language (ASL) from birth have been shown
to acquire ASL at the same rate that hearing children develop spoken
language.
- There are many degrees, types, and patterns of hearing
loss. There is no one description or profile of a deaf or hard of
hearing that fits all children.
- Even if two children have the same degree, type and
pattern of hearing loss, it does not mean they hear and understand
the same thing or benefit from a hearing aid in the same way. Each
child's hearing and speaking capabilities are unique.
- Some causes of deafness (i.e.: rubella, cytomeglovirus,
meningitis, etc...) have other associated conditions that may impact
on a child's learning characteristics.
- Many deaf children have some residual (remaining)
hearing.
|
Developed by: Debra
Nussbaum, Audiologist, Kendall Demonstration Elementary
School
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